Priority 10 from the Rare Musculoskeletal Diseases in Adulthood PSP
|UNCERTAINTY: What are the best ways to prevent dental problems in people with rare metabolic bone disorders? (JLA PSP Priority 10)
|JLA question ID
|Not available for this PSP
A prospective study reported that dental abnormalities were common in XLH, unrelated to delayed medical treatment. The authors recommended regular oral examination (Souza MA et al, Clinics (Sao Paulo) 2010, 65: 1023-1026). Small case series suggest that duration of tretment with activated vitamin D supplements may be associated with a beneficial effect on dental health (Chaussain-Miller C et al, J Pediatr 2003; 142: 324-331, Connor J et al, J Clin Endocrinol Metab 2015; 100: 3625-3632).
|Health Research Classification System category
|Extra information provided by this PSP
|Original uncertainty examples
|Is there any prophylactic treatment other than good oral hygiene to prevent dental infections? ~ Is there any preventive dental treatment advice? ~ Are there any procedures that a dentist might suggest to a non XLH person that would not be appropriate to the an XLH patient? eg deep cleaning, whitening?
|Individual survey submissions categorised by Health or Social Care Professionals, Organisations representing people with rare musculoskeletal diseases, people with rare musculoskeletal diseases, relatives/carers/friends, Other. For full details of the type of submitter for each individual question, please see the spreadsheet of data held on the JLA website.
|PSP unique ID
|Rare Musculoskeletal Diseases in Adulthood
|Total number of uncertainties identified by this PSP.
|39 (To see a full list of all uncertainties identified, please see the detailed spreadsheet held on the JLA website)
|Date of priority setting workshop
|18 June 2018