Priority 8 from the Liver Glycogen Storage Disease (International) PSP

UNCERTAINTY: How to manage diet regimen in relation to "before, during and after" physical exercise (sport, playing) for patients with liver Glycogen Storage Disease?  (JLA PSP Priority 8)
Overall ranking 8
JLA question ID 0090/8
Explanatory note

Glucose homeostasis in liver GSD can be challenging under conditions that require more energy, such as physical exercise. This question focusses on optimal management of the diet in relation to physical exercise. 


For details of the evidence checked, please see the spreadsheet held on the JLA website.

Health Research Classification System category Metabolic and endocrine 
Extra information provided by this PSP
Original uncertainty examples Are there studies on the subject of sport, which sports / duration help to improve the metabolism? ~ If he starts doing sports/swimming, what does that do with his diet? ~ What time before exercise should I give cornstarch and protein?  
Submitted by Patient, carer and healthcare professionals 
PSP information
PSP unique ID 0090
PSP name International Glycogen Storage Disease PSP
Total number of uncertainties identified by this PSP 72  (To see a full list of all uncertainties identified, please see the detailed spreadsheet held on the JLA website)
Date of priority setting workshop 24 May 2019