Priority 17 from the Liver Glycogen Storage Disease (International) PSP
|UNCERTAINTY: How can patients with liver Glycogen Storage Disease achieve and/or maintain a healthy weight throughout life? (JLA PSP Priority 17)|
|JLA question ID||0090/17|
Weight gain can be a complication of liver GSD since the cornerstone of treatment is a diet rich in complex carbohydrates. This question emphasized that more research is necessary on protocols to prevent, achieve or maintain a healthy weight, without metabolic derangement occuring due to undertreatment.
For details of the evidence checked, please see the spreadsheet held on the JLA website.
|Health Research Classification System category||Metabolic and endocrine|
|Extra information provided by this PSP|
|Original uncertainty examples||Development of overweight and diabetes at an adult age. ~ The weight gain that comes with consuming cornstarch ~ Is there a possibility to lose weight despite the high carbohydrates?|
|Submitted by||Patient, carer and healthcare professionals|
|PSP unique ID||0090|
|PSP name||International Glycogen Storage Disease PSP|
|Total number of uncertainties identified by this PSP||72 (To see a full list of all uncertainties identified, please see the detailed spreadsheet held on the JLA website)|
|Date of priority setting workshop||24 May 2019|