Priority 14 from the Liver Glycogen Storage Disease (International) PSP

UNCERTAINTY: How to prevent and/or treat neurological problems in patients with liver Glycogen Storage Disease?  (JLA PSP Priority 14)
Overall ranking 14
JLA question ID 0090/14
Explanatory note

As a result of acute and chronic periods of hypoglycemia in liver GSD, neurological symptoms can occur. This question emphasizes that more research is necessary to avoid these neurological complications. 


For details of the evidence checked, please see the spreadsheet held on the JLA website.

Health Research Classification System category Metabolic and endocrine 
Extra information provided by this PSP
Original uncertainty examples How do we follow neurologic sequele and developement? ~ How do we monitor neurologic sequele and developement? 
Submitted by Patient, carer and healthcare professionals 
PSP information
PSP unique ID 0090
PSP name International Glycogen Storage Disease PSP
Total number of uncertainties identified by this PSP 72  (To see a full list of all uncertainties identified, please see the detailed spreadsheet held on the JLA website)
Date of priority setting workshop 24 May 2019